| Title | Esophageal perforation in recessive dystrophic epidermolysis bullosa. |
| Publication Type | Journal Article |
| Year of Publication | 1994 |
| Authors | Horan TA, Urschel JD, MacEachern NA, Shulman B, Crowson AN, Magro C |
| Journal | Ann Thorac Surg |
| Volume | 57 |
| Issue | 4 |
| Pagination | 1027-9 |
| Date Published | 1994 Apr |
| ISSN | 0003-4975 |
| Keywords | Adult, Diatrizoate Meglumine, Epidermolysis Bullosa Dystrophica, Esophageal Perforation, Esophagectomy, Esophagus, Follow-Up Studies, Food, Foreign Bodies, Humans, Male, Radiography, Reoperation |
| Abstract | Recessive dystrophic epidermolysis bullosa is an inherited mechanobullous disease characterized by skin blistering and esophageal bullae. In response to minor trauma, a split in the dermis or esophageal subepithelium occurs. Esophageal perforation is a rare complication. Because the esophagus is diseased in these patients, we believe that esophagectomy rather than repair is the treatment of choice for esophageal perforations. We report a patient for whom early primary repair failed and esophagectomy was required. |
| DOI | 10.1016/0003-4975(94)90234-8 |
| Alternate Journal | Ann Thorac Surg |
| PubMed ID | 8166505 |
Related Faculty:
Cynthia M. Magro, M.D.